Abstract
Scimitar syndrome is a rare condition including right lung hypoplasia, anomalous pulmonary venous drainage, dextroposition of the heart, and hypoplastic right pulmonary artery (RPA). The infantile form is sometimes associated with pulmonary hypertension, cardiac failure, and a poorer prognosis. We present a 1-day-old girl with a rare combination of partial left pulmonary artery (LPA) sling and scimitar syndrome, which was suspected in prenatal sonography and confirmed by echocardiography, computed tomography and cardiac catheterization. The patient received re-implantation of the aberrant left lower pulmonary artery and patch augmentation of the main-left upper pulmonary arteries at 4 months of age. Another operation was performed at 7 months of age with patch augmentation for stenosis of the left lower pulmonary artery and left pulmonary vein elevation to relieve its clenching of the left lower bronchus, with improvement of respiratory distress.
Sign-in/Register to access full text options 
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callDisclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
