Abstract
A 3 year-old girl with recurrent chest infections had chest radiograph showing the typical “Turkish sword” sign which could be found in 70% in the childhood-adult group of Scimitar syndrome, a rare form of partial anormalous pulmonary venous drainage (PAPVD) associated with hypoplastic lung. The anomalous pulmonary veins drain into the systemic venous system such as inferior vena cava (IVC), right atrium, hepatic or portal vein.
Highlights
The reconstructed Computerized Tomography (CT) images of thorax in this patient demonstrated a few unusual features of the rare condition: 1) Anomalous right pulmonary veins joined the inferior vena cava (IVC) was interrupted after coursing through the liver (Figure 1b)
Similar to two reported cases [2,3], the IVC was interrupted and the dilated azygos and hemiazygos veins received venous blood from the anomalous scimitar vein and all infradiaphragmatic systemic return except the hepatic vein which was draining to the right atrium separately
Scimitar syndrome with various complex vascular connections and pulmonary malformations are described in literature, the embryological development of the congenital abnormalities is still not well defined
Summary
The reconstructed Computerized Tomography (CT) images of thorax in this patient demonstrated a few unusual features of the rare condition: 1) Anomalous right pulmonary veins joined the inferior vena cava (IVC) was interrupted after coursing through the liver (Figure 1b). 2) Azyos and hemiazygos veins were dilated (Figure 1d).
Sign-in/Register to view highlights & summary Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callDisclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
