Abstract
Turner syndrome is known to be associated with significant cardiovascular abnormalities in 23-45%. Scimitar syndrome is a rare congenital anomaly characterized by anomalous connection of the pulmonary veins to the inferior vena cava. It represents 3-5% of all partial anomalous pulmonary venous return (PAPVR). We report a rare case of Scimitar syndrome in a child with Turner Syndrome. Sri Lanka Journal of Child Health , 2015; 44 (2): 107-109
Highlights
Turner syndrome is known to be associated with significant cardiovascular abnormalities in 23-45%1
Thoracic angiography revealed partial anomalous pulmonary venous return (PAPVR) with right, lower pulmonary vein draining into the inferior vena cava [IVC] (Figure 1)
Scimitar syndrome is a rare congenital cardiopulmonary anomaly seen in 3-6% of patients with PAPVR2
Summary
Turner syndrome is known to be associated with significant cardiovascular abnormalities in 23-45%1. Scimitar syndrome is a rare congenital anomaly characterized by anomalous connection of the pulmonary veins to the inferior vena cava. It represents 3-5% of all partial anomalous pulmonary venous return (PAPVR)[2]. We report a rare case of Scimitar syndrome in a child with Turner Syndrome
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