Sarcoma fibromixoide de bajo grado con metástasis pulmonares. Reporte de un caso raro

Abstract

Background Low-grade fibromyxoid sarcoma is a very rare tumor that tends to develop in deep soft tissues of young adults and has the potential for local recurrence and distant metastasis. Clinical case We present the case of a 36-year-old man with a low-grade fibromyxoid sarcoma in the right shoulder, which was initially reported as a 4-year-old tumor, undergoing extensive resection with a histopathological report of low-grade fibromyxoid sarcoma, whose deep surgical edge was in bony contact. A simple and contrasted axial tomography was performed where an 8 mm left lung lesion was observed in the upper lobe lower lingular segment of heterogeneous content, hyperdense with contrast medium reinforcement. Left lateral thoracotomy is performed for metastasectomy and pathology corroborates the diagnosis of metastasis from fibromyxoid sarcoma. Conclusion Low histological fibromyxoid sarcoma is a very rare tumor that must be differentiated from other soft tissue tumors. Recurrences and metastases are reported, despite short or prolonged disease-free periods of up to 50 years, so patients with a history of this tumor should be followed up.