Ruptured, fusiform, distal lenticulostriate aneurysm causing intraventricular haemorrhage in a patient with antiphospholipid-negative Sneddon's syndrome

Abstract

Sneddon’s syndrome (SS) is a rare, non-inflammatory, occlusive, rterial vasculopathyaffecting small tomediumcalibrearterial vesels and defined by the presence of bluish-purple, lattice-like skin esions known as livedo racemosa in association with ischaemic erebrovascular events. Predominantly affecting women in early iddle age [1]. SS occurs both sporadically and in a familial form nd is often accompanied by hypertension and cardiac valvuopathies [1]. Anti-phospholipid antibodies (aPL) are detected in roundhalf of cases [1] andderangement of clotting factors has also een reported. While abnormalities on cerebral digital subtraction ngiography (DSA) in SS are common and diverse [1,2], intracranial neurysms have not, so far, been recognised as a feature. Aneurysms arising from distal branches of the lenticulostriate rteries are exceedingly rare [3,4]. We report a case of a fusiform, istal lenticulostriate artery aneurysm presenting with intravenricular haemorrhage (IVH) in a patient with SS – the first report of uch an association.