Right ventricular function and adaption after hemi-Fontan completion in children with hypoplastic left heart syndrome

Bram Ruijsink,Reza Razavi,Kuberan Pushparajah,Hannah Bellsham-Revell

doi:10.1186/1532-429x-18-s1-p161

Abstract

Background The systemic right ventricle (RV) in patients with hypoplastic left heart syndrome (HLHS) is prone to failure. The complex geometry and contraction pattern of the systemic RV makes identification of patients at risk for failure challenging, especially in the light of radical changes in loading conditions during staged palliation. MRI allows for accurate quantification of cardiac volumes and provides assessment of the whole heart without restrictions in imaging planes. Recent advances in cardiac MRI analysis software allows for quantification of regional deformation from conventional balanced steady state free precession cine images. We sought to investigate changes in ventricular function before and after the hemi-Fontan (HF).

Highlights

The systemic right ventricle (RV) in patients with hypoplastic left heart syndrome (HLHS) is prone to failure
The volume unloading during HF surgery resulted in a decrease in end-diastolic and end systolic volumes (p
Both changes in global radial and circumferential strain correlated with EF whereas longitudinal strain did not

Summary

Background

The systemic right ventricle (RV) in patients with hypoplastic left heart syndrome (HLHS) is prone to failure. The complex geometry and contraction pattern of the systemic RV makes identification of patients at risk for failure challenging, especially in the light of radical changes in loading conditions during staged palliation. MRI allows for accurate quantification of cardiac volumes and provides assessment of the whole heart without restrictions in imaging planes. Recent advances in cardiac MRI analysis software allows for quantification of regional deformation from conventional balanced steady state free precession cine images. We sought to investigate changes in ventricular function before and after the hemi-Fontan (HF)

Methods

Results

Conclusions