Right sided facial nevus with contralateral cavernous angioma in a child with Sturge Weber syndrome

Abstract

Sturge Weber syndrome is a rare sporadic neurocutaneous syndrome. It has extra -oral manifestations mostly in form of unilateral port wine stain on face that are ipsilateral to intra-cranial lesions (mostly lepto-meningeal angioma), seizures, glaucoma and intra-orally by hemangioma of ipsilateral gingiva. We case report a child with Sturge Weber syndrome with facial nevus opposite to intra-cranial lesion, intra-oral port wine stain and gum hypertrophy. Other than contralateral intracranial lesion and facial nevus, challenge was whether to see gingival manifestations as part of syndrome or as drug side effect, as child was also on phenytoin, an anti-epileptic drug widely related to this condition.