Abstract
We are going to report a rare association of dilated cardiomyopathy with Wilms tumour in 2-year old female child. The patient was given neo-adjuvant chemotherapy leading to reduction in size of primary tumour with subsequent improvement in cardiac function. The patient subsequently underwent right nephrectomy with return of cardiac function to normal.
Highlights
Compression on renal hilar vessels leads to hypertension which could lead to congestive heart failure
In 2003, 2 cases of nephroblastoma with dilated cardiomyopathy without hypertension were reported by Trebo et. al[5]
The patient was treated with neoadjuvant chemotherapy which led to regression in tumour burden
Summary
Wilms tumour (nephroblastoma) constitutes the most common paediatric renal tumour accounting for 80-90% of paediatric renal tumors and 12 percent of childhood cancers. It is rare during the first year of life and is commonly seen between 1-5 years of age with a peak incidence at 3 years[1]. Wilms tumour usually presents with slow growing abdominal mass. Cardiovascular complications of Wilms tumour are well known and include congestive cardiac failure (due to hypertension caused by the pressure of the tumour on hilar or intra-renal vessels) or intra-cardiac extension of a tumour thrombus. CASE HISTORY Two year-old female child presented to out-patient department with abdominal distension, episodic respiratory distress and decreased food intake for last 1 month. The child was awake, febrile (38 o C)with blood pressure 88/48 mm Hg.Her weight was 11 kg
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