Reversible Cerebral Vasoconstriction Syndrome Associated with a Suprarenal Mass.

Camila Pantoja-Ruiz,Andrés Ricaurte-Fajardo,María Isabel Ocampo-Navia,Juliana Coral-Casas

doi:10.14712/23362936.2020.9

Abstract

Reversible cerebral vasoconstriction syndrome (RCVS) is characterised by severe thunderclap headaches (with or without the presence of acute neurological symptoms) and segmental vasoconstriction of cerebral arteries that resolves spontaneously in a period of three months. Cases have been described in the literature with producing and non-producing masses of metanephrines. Within these reports, associations with cavernous haemangioma, medulloblastoma, colon cancer, paraganglioma, pheochromocytoma, uterine fibroids, among others were found. However, no association with adrenal masses which do not produce metanephrines was found. In this context, we reported the case of a woman with this type of tumour associated with RCVS which provided a treatment challenge, as well as we reviewed the literature on cases of RCVS associated with masses.

Highlights

We reported the case of a woman with this type of tumour associated with Reversible cerebral vasoconstriction syndrome (RCVS) which provided a treatment challenge, as well as we reviewed the literature on cases of RCVS associated with masses
Thunderclap headache is usually the typical symptom with or without neurological focalization and the diagnostic criteria suggested by Calabrese et al (2007) propose that headache should be associated with diffuse changes in the tone of the cerebral vasculature documented by angiography (De Angelis et al, 2018; Arenas-Beltrán et al, 2019)
Because it is usually associated with medical conditions, a classification dividing the aetiology of the syndrome between idiopathic and symptomatic has been purposed (Coral and Roa, 2009)

Summary

Reversible Cerebral Vasoconstriction Syndrome Associated with a Suprarenal Mass

Camila Pantoja-Ruiz1, Andrés Ricaurte-Fajardo2, María Isabel Ocampo-Navia2, Juliana Coral-Casas1 1Neuroscience Department, Hospital Universitario San Ignacio, Pontificia Universidad Javeriana, Bogotá, Colombia; 2Medical School, Pontificia Universidad Javeriana, Bogotá, Colombia Received November 17, 2019; Accepted May 28, 2020. Key words: Reversible cerebral vasoconstriction syndrome – Headache – Cerebral angiography – Tumour

Introduction

Reversible Cerebral Vasoconstriction Syndrome

Findings

Discussion