Abstract
A3-month-old baby (born 36/40weeks)with antenatal diagnosis of tuberous sclerosis (TS) (having cardiac rhadomyomas and multiple subependymal nodules) was admitted with new onset infantile spasms. Electroencephalography revealed modified hypsarrhythmia. The spasms were managedwith Vigabatrin. Magnetic resonance imaging of the brain reveadled multiple subependymal and subcortical tubers scattered throughout both cerebral hemispheres in keeping with TS (Figs 1a and 1b). Two very tiny retinal masses, hypointense on T2-weighted images and moderately enhancing on post gadolinium T1-weighted images were noted within the left eye, suggestive of astrocytic hamartomas (Figs 2 and 3). Thesefindingswere further confirmed with orbital ultrasound that revealed welldefined retinal masses in left eye (Fig. 4). Ophthalmic examination under anesthesia confirmed multiple retinal astrocytic hamartomas in left eye. Her recent ophthalmic examination, at the age of 2 years demonstrated stable appearance of the retinal lesions. Retinal astrocytic hamartomas are known ocular manifestation of TS complex [1]. The largest reported
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