Repair of complete atrioventricular canal in early childhood.

Abstract

From November 1977 to January 1981, 10 consecutive patients underwent intracardiac repair of the complete atrioventricular canal at our institution. Ages ranged from 14 months to 4.5 years (mean age 20 months). Four patients were predominantly of type A, while 6 were predominantly of type C according to Rastelli's classification. Three patients had associated cardiac anomalies (2 tetralogy of Fallot and one parachute mitral valve). Standard repair and correction of the associated anomalies were performed under cold cardioplegic cardiac arrest and deep hypothermia with low-flow perfusion or circulatory arrest. Two patients died early postoperatively in severe renal failure and one died 6.5 months postoperatively in cardiac failure due to progressive mitral valve incompetence. One patient, with parachute mitral valve, was reoperated and the mitral valve was replaced because of persistent mitral insufficiency. The patients were followed up for a period of 4 to 35 months (mean 14 months) with a total of 112 patient months. The result of the operation was very good and all patients with retarded growth curve preoperatively showed a marked acceleration of their growth curve after operation. The operative results in this group of patients are independent of age and weight at the time of operation but appear to be influenced by associated cardiac anomalies and by the quality and quantity of atrioventricular valve tissue available for reconstruction.