Abstract
Hereditary hemorrhagic telangiectasia (HHT) is caused by an autosomal dominant gene and characterized by multiple arteriovenous malformations in several organs, leading to bleeding or shunting. These patients often suffer severe infections and heart failure, which should be managed in the perioperative period, when open heart surgery is indicated. We report a case of successful aortic root replacement for active prosthetic valve endocarditis and ventricular septal perforation in a patient with HHT, who had severe heart failure.
Highlights
Hereditary hemorrhagic telangiectasia (HHT), an autosomal dominant genetic disorder, is characterized by multiple organ involvements such as cutaneous or mucosal telangiectasia and visceral multiple arteriovenous malformations (AVMs), which develop in the brain, liver, or lungs
We report a case of successful aortic root replacement for active prosthetic valve endocarditis and ventricular septal perforation in a patient with HHT, who had severe heart failure
The cutaneous or mucosal telangiectasia and AVM associated with HHT can cause multiple complications, which are difficult to manage, and may result in life-threatening events perioperatively
Summary
Redo cardiac surgery for active prosthetic valve endocarditis associated with hereditary hemorrhagic telangiectasia: report of a case. This article is published with open access at Springerlink.com
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