Abstract
IntroductionDermatofibrosarcoma protuberans is an uncommon low-grade soft tissue sarcoma with a high potential for recurrence as it has irregular finger like extensions.Case descriptionWe report a case of a large, recurrent dermatofibrosarcoma protuberans in a child involving the anterior abdominal wall, which posed a challenge for reconstruction. Peritoneum sparing full thickness resection of the anterior abdominal wall, meshplasty and a free anterolateral thigh flap was performed for reconstruction of the defect.Discussion and evaluationLarge composite defect, involving more than half of the anterior abdominal wall, necessitate a free flap reconstruction. Although these reconstructions are technically challenging in children, they are the only option available.ConclusionComplete surgical excision is essential for DFSP of the abdominal wall, which may result in large challenging defects. Free flaps remain the only option in this scenario and hence it is essential to have expertise for microvascular flap reconstruction.
Highlights
Dermatofibrosarcoma protuberans is an uncommon low-grade soft tissue sarcoma with a high potential for recurrence as it has irregular finger like extensions.Case description: We report a case of a large, recurrent dermatofibrosarcoma protuberans in a child involving the anterior abdominal wall, which posed a challenge for reconstruction
Complete surgical excision is essential for Dermatofibrosarcoma protuberans (DFSP) of the abdominal wall, which may result in large challenging defects
Free flaps remain the only option in this scenario and it is essential to have expertise for microvascular flap reconstruction
Summary
Complete surgical excision is essential for DFSP of the abdominal wall which may result in large challenging defects. Free flaps remain the only option in this scenario and it is essential to have expertise for microvascular flap reconstruction. Author details 1 Division of Pediatric Surgical Oncology, Department of Surgical Oncology, Tata Memorial Centre, Ernest Borges Road, Parel, Bombay 400012, India. 2 Department of Plastic and Reconstructive Surgery, Tata Memorial Centre, Bombay, India. Authors’ contributions SQ performed the surgical resection with the assistance of KCV and MB. KCV drafted the manuscript with the assistance of MB. All authors were involved in review of literature. All authors read and approved the final manuscript
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