Rare Case of Susac Syndrome

Abstract

Susac syndrome is a rare autoimmune disease affecting the precapillary arteries of the brain, eye and ears causing encephalopathy, branch retinal artery occlusion and sensorineural hearing loss. It is underdiagnosed as it rarely presents with the classic triad. Encephalopathy and branch retinal artery occlusion are curable if the treatment is started early, however the sensorineural hearing loss may be irreversible. The disease course may be monocyclic, polycyclic or chronic. In this review present a case of Susac which was not diagnosed until late in the disease course. Even though the three criteria manifested clinically, the patient was successfully treated. We will also provide a clinical review on the disease based on our research from the literature