Rare case of anomalous right coronary artery from pulmonary artery (ARCAPA syndrome)

Abstract

Anomalous right coronary artery from pulmonary artery (ARCAPA) is a rare congenital anomaly of right coronary artery, most of the patient are asymptomatic, although myocardial infarction and sudden cardiac arrest has been reported. Herein we present a 5 month old infant presented with chest infection, during routine examination cardiac murmur detected, anomalous right coronary artery from pulmonary artery suspected by transthoracic Echocardiography which showed dilated (4mm) left main stem of coronary artery with mild left ventricular dilatation, but the origin of right coronary artery couldn’t be detected. Coronary angiography done which confirm the diagnosis and the child successfully operated on for reimplantation of right coronary artery to the aortic cusp.