Radiographic appearance of the thorax in systolic click-late systolic murmur syndrome

Abstract

The posteroanterior and lateral chest X-ray films of 64 consecutive patients with an isolated systolic click (55 patients) or a systolic click with a late systolic murmur (9 patients) showed a striking frequency of thoracic skeletal abnormalities. There were 50 female and 14 male subjects. The average age of the female subjects was 36.7 years (range 13 to 67), that of the male subjects 39.7 years (range 17 to 56). Seventy-two percent of the female and 78 percent of the male subjects had an anteroposterior/transverse thoracic ratio less than the mean ratio in a normal population. Bony abnormalities such as pectus excavatum, straight thoracic spine and scoliosis occurred alone or in combination in 31 of the 50 female patients (62 percent) and in 8 of the 14 male patients (57 percent). Overall, 39 of the 64 patients (61 percent) had at least one of the skeletal abnormalities. Scoliosis occurred in 25 subjects (39 percent) and was mild in 19. A “straight back” was found in 15 (23 percent) and pectus excavatum in 7 patients (11 percent). The explanation for these findings is not apparent. Thoracic cage abnormalities should be included as one of the nonauscultatory features of the systolic click-late systolic murmur syndrome.