Abstract
Pulmonary hypertension: the importance of amultidisciplinary approach.
Highlights
Pulmonary hypertension (PH) can be found in different clinical conditions and is categorised into five groups based on a similar presentation, haemodynamic profile, pathological findings, and treatment: pulmonary arterial hypertension (PAH), PH based on left heart disease, PH due to lung disease and/or hypoxaemia, chronic thromboembolic PH (CTEPH), and PH with unclear and/or multifactorial mechanisms [1, 2]
Patients with congenital heart disease (CHD) with a prevalent or corrected systemic-to-pulmonary shunt are at risk for the development of PAH [3]
One of the best examples of a disease associated with PH based on a multifactorial aetiology is sarcoidosis, a rare multisystemic disorder characterised by non-caseating granulomas that can present in multiple tissues
Summary
PH can be found in different clinical conditions and is categorised into five groups based on a similar presentation, haemodynamic profile, pathological findings, and treatment: pulmonary arterial hypertension (PAH) (group 1), PH based on left heart disease (group 2), PH due to lung disease and/or hypoxaemia (group 3), chronic thromboembolic PH (CTEPH) (group 4), and PH with unclear and/or multifactorial mechanisms (group 5) [1, 2]. Patients with congenital heart disease (CHD) with a prevalent or corrected systemic-to-pulmonary shunt are at risk for the development of PAH [3]. Up to 70 % of patients with severe chronic heart failure suffered from PH [5], whereas the prevalence of pulmonary arterial hypertension (PAH) is estimated to be between 15 and 60 patients per million population [6].
Sign-in/Register to view highlights & summary Sign-in/Register to access full text options 
Free) 
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a call
