Pulmonary Artery Sling, Congenital Blindness and Basal Ganglia Hemorrhage: A Fortuitous Association?

Abstract

Pulmonary artery sling (PAS) is a rare congenital vascular anomaly that typically presents in the first month of life with severe respiratory symptoms. A small subset of patients with this anomaly survives to adulthood with few or no symptoms. Several associated congenital anomalies were described. In this article, we describe an incidental finding of an asymptomatic PAS in an adult patient with congenital anisocoria and blindness 2 years after a spontaneous intracerebral hemorrhage. To the best of our knowledge, this is the first report on this association in an elderly patient. We believe that its documentation might contribute to a better understanding of this anomaly and its implications. J Med Cases. 2014;5(1):34-35 doi: http://dx.doi.org/10.4021/jmc1617w