Pulmonary arterial hypertension: diagnosis and treatment

Abstract

Pulmonary arterial hypertension is one of the clinical groups of arterial hypertension. It is a rare, chronic disease with a very poor prognosis. Diagnostic procedures ruling out different causes of present symptoms and other forms of pulmonary hy pertension are difficult and specific. Current European guidelines recommend combined treatment with endothelin recep tor antagonist, prostanoids, and phosphodiesterase type 5 inhibitors.