Abstract
30Mar 2017 PULMONARY ALVEOLAR MICROLITHIASIS: CLINICAL AND RADIOPATHOLOGICAL REVIEW. Tushar Sahasrabudhe and Sowmya Attipatla. Department of Pulmonary medicine, Dr. D.Y.Patil Medical college and Research institute, Pimpri, Pune.
Highlights
Pulmonary alveolar microlithiasis (PAM) is a rare and slowly progressive diffuse chronic lung disease characterized by deposition of small calcium phosphate spherules within the alveolar cavity.(1) The etiology of the disease is still unknown and is supposed to be due to defect in the inherited local enzyme that is responsible for calcium deposition.(2)The disease is usually seen from birth up to 40 years of age.(1,3) Clinically, the disease course is different
Grade I MMRC dyspnea progressed to grade II MMRC on presentation, over 3 years
On chest x-ray (Fig-1) diffuse, dense, large calcifications noted in bilateral lung fields
Summary
Pulmonary alveolar microlithiasis (PAM) is a rare and slowly progressive diffuse chronic lung disease characterized by deposition of small calcium phosphate spherules within the alveolar cavity.(1) The etiology of the disease is still unknown and is supposed to be due to defect in the inherited local enzyme that is responsible for calcium deposition.(2)The disease is usually seen from birth up to 40 years of age.(1,3) Clinically, the disease course is different. Most of the patients are asymptomatic or having very mild symptoms and majority of patients either having normal or restrictive pulmonary function tests.
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