Abstract
Pseudotumor is a rare complication of hemophilia with a prevalence 1–2% of all clinical cases. Commonly bone lesions affect long tubular bones, the pelvis, wrist and foot bones. According to world science literature only 16 cases of maxilla bone lesions in patients with hemophilia were found. This article describes a clinical case of maxilla pathological lesion with the destruction of facial skeleton bones in a one year old boy. The differential diagnosis included malignant and benign neoplasia, inflammatory processes. During laboratory examination a deficiency of IX coagulation factor was revealed and the patient was diagnosed with hemophilia В. The patient underwent surgical treatment by removing the lesion with specific replacement therapy; an intraosseous organizing hematoma was verified. The maxilla pseadotumor in this child was a manifestation of hemophilia. The patient's parents agreed to use the information, including the child's photo, in scientific research and publications.
Highlights
ФГБУ «Национальный медицинский исследовательский центр детской гематологии, онкологии и иммунологии им
Pseudotumor is a rare complication of hemophilia with a prevalence 1–2% of all clinical cases
This article describes a clinical case of maxilla pathological lesion with the destruction of facial skeleton bones in a one year old boy
Summary
Псевдоопухоль верхней челюсти у ребенка первого года жизни как первое проявление гемофилии В. Контактная информация: Калинина Маргарита Павловна, врач-оториноларинголог отделения онкологии и детской хирургии ФГБУ «НМИЦ ДГОИ им. В мировой литературе описано 16 пациентов с поражением в области верхней челюсти при гемофилии. ПО верхней челюсти у ребенка была первым проявлением гемофилии. According to world science literature only 16 cases of maxilla bone lesions in patients with hemophilia were found. This article describes a clinical case of maxilla pathological lesion with the destruction of facial skeleton bones in a one year old boy. Наиболее часто ПО поражает длинные трубчатые кости, кости таза, кистей и стоп, локализация в челюстно-лицевой области встречается крайне редко [3]. Опубликовали статью, в которой проанализировали 16 случаев развития ПО в челюстно-лицевой области при гемофилии.
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