PROSTHETIC TREATMENT OF A PATIENT WITH NAGERACROFACIALDYSOSTOSIS: A CASE REPORT

Abstract

Introduction: Nager syndrome, alsoknown as Nager acrofacialdysostosis, was first described by Nager and de Reynierin 1948. It is a rare syndrome resultingfromdevelopmentalabnormalities of the first and second branchial arches and ismostlysporadic. The prevalenceisunknown about 100 cases have been published up to now. The purpose of this report is to present a case of Nager syndrome wherewewere able to achieve a conventionalcomplete denture despite the many challenges due to the complexity of the clinical case. Case Report: A 27-years-old female patient wasreferred to our service of RemovableProsthodontics at Casablanca UniversityHospital Center complaining of difficulty in speaking and chewing. The patient presentedseveralcraniofacial anomalies including facial atrophy, maxillomandibularhypoplasia, flat nasal bridge, associated to defectsupper and lowerlimbs. Based on these craniofacial characteristics and the coexistingupper and lowerlimbpreaxial anomalies, a diagnosis of Nager syndrome wasconfirmed.The intra-oral examinationrevealed an edentulous mandibular arch and carious, mobile and hypomineralizedmaxillaryteeth, the patient presents a severemicrognatiawith a skeletal Cl III whichcomplicates the prosthetic management of the patient. Therealization of a complete denture has improved the comfort and function of the patient. Conclusion: Nager Syndrome is a condition with a ratherheavyclinical situation and its management must bemultidisciplinary, the psychology and comfort of these patients isoftenaffected. Oral care has improvedaesthetics, function and the quality of life in this patient with Nager syndrome.