Abstract
BackgroundEctodermal dysplasia is a rare genetic disorder that affects ectodermally derived structures, including teeth, nails, hair, and sweat glands. Hypohidrotic ectodermal dysplasia is the most common type, with oligodontia being the most striking dental feature. Prosthetic rehabilitation in children with ectodermal dysplasia is an important step toward improving their overall quality of life. The fixed prosthesis has the advantages of being more stable in the mouth with good child compliance and a good aesthetic outcome.Case presentationOur patient was a 5-year-old Middle Eastern boy with oligodontia caused by ectodermal dysplasia. He was managed by fabrication of an upper functional space maintainer and a lower fixed partial denture to restore occlusion, masticatory function, aesthetics, and overall quality of life.ConclusionsThe use of the fixed prosthesis in children is a new and evolving treatment modality that resolves many of the issues caused by removable prostheses. It accommodates jaw growth in the mandible, reduces the need to remake the prosthesis, and has an overall better aesthetic outcome.
Highlights
Ectodermal dysplasia is a rare genetic disorder that affects ectodermally derived structures, including teeth, nails, hair, and sweat glands
More than 170 types are described in the literature [1], but the common ones are hypohidrotic and hidrotic, which differ in the degree of sweat gland function and hereditary pattern
Hypohidrotic Ectodermal dysplasia (ED) is characterized by hypohidrosis due to the absence of or reduction in the number of sweat glands, hypotrichosis, and hypodontia [2]
Summary
The use of the fixed prosthesis in children is a new and evolving treatment modality that resolves many of the issues caused by removable prostheses.
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