Proboscis Lateralis : Report Of One Congolese Case

Abstract

Introduction: Proboscis lateralis is known as a rare anomaly related to facial fusion defect. The optimal care of the patient with a multidisplinary approach that may involve an ophthalmologist, plastic surgeon, oro-maxillofacial surgeon or otolaryngologist has necessary.Case-report: It's a case note ofa 1 day-old female infant was consulted into our department because of the complaint of nasal anomaly. The physical examination revealed a tubular structure originated from the medial canthal region, an absent left nasal structure or right heminasal hypoplasia with a normal right nasal structure. According to those signs, the diagnostic of proboscis lateralis was given.Discussion: PL is known as a rare anomaly related to facial fusion defect.The precise embryologic mechanism responsible for the development of PL has not been defined.Nowadays, it does not seem to be any racial predilection in proboscis lateralis.In this case, it is very difficult to prove the association between: the embryologic mechanism of PL, the bad follow up of pregnancy, and the prenatal history of exposure to alcohol, drugs auto medicationConclusion: Ignorance and poor management, and lack of equipment yield impossible the care of proboscis lateralis's patient in our context.