PRIMITIVE BLASTOMA PERIPHERAL PRIMITIVE NEUROECTODERMAL TUMOR OF THE MANDIBLE

Abstract

Peripheral primitive neuroectodermal tumors (pPNET) are high-grade malignant tumors seen in the early age group {5-25 year}, primarily affecting long bones of extremities afterwards the pelvis, ribs and vertebrae. pPNET in the mandible (head & neck) accounts for only 2% of the reported cases. pPNET agitate difculty in arriving at a diagnosis due to poor differentiation of small round cells and could be established only by histopathology and immunochemistry. Surgery with chemotherapy is the preferrable treatment of choice in the mandible. In this article, we describe a rare case of PNET of the mandible in 11-year-old boy and review of literature.