Abstract
Primary proliferative pulmonary vascular sclerosis is rare. Brenner,<sup>1</sup>in an exhaustive study of the pathology of the vessels of the pulmonary circulation and with an excellent review of the literature, could find but 16 well described cases, including 1 of his own, that could be accepted without reserve. In all other cases appeared some factor, such as chronic cardiac or pulmonary disease, that was thought capable of causing secondary sclerosis, either severe or in mild form. It seems obvious that the latter cases fall into that group reported in the literature as cases of Ayerza's disease<sup>2</sup>or syndrome, as in all of these the condition was obviously secondary vascular sclerosis of the pulmonary artery. Without exception it was associated with chronic bronchopulmonary or cardiac disease.<sup>3</sup>This is true also of the cases recently described by Kaump and Dry.<sup>4</sup>MacCallum<sup>5</sup>found but 1 case of primary
Sign-in/Register to access full text options 
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a call
