Primary CNS Sarcomas in Pediatric Patients: Radiologic Features

Abstract

Primary CNS sarcomas are rare yet very aggressive tumors associated with high morbimortality rates. There is scarce literature about their radiologic characteristics. This retrospective study aimed to describe the clinical, pathologic, and imaging characteristics of these neoplasms. Twenty-four patients treated in a pediatric oncology referral center were recruited between 2008 and 2021. Their medical records were reviewed, and the pathology samples and images (CT and MR imaging) were analyzed. Most of the tumors were supratentorial, unifocal, solid lesions associated with postcontrast enhancement and diffusion restriction. The main manifestation was intracranial hemorrhage. A higher percentage of tumor resection and lower relapse rates were the main prognostic features found.