Primary ciliary dyskinesia in children

Abstract

Primary ciliary dyskinesia is characterized by impaired mucociliary clearance and contributes to the recurrence of recurrent and chronic upper and lower respiratory tract infections. In this paper we elucidated a clinical case confirmed in the Pneumology Clinic of the Institute of Mother and Child, where he was investigated by ECG, pulmonary Rg, pulmonary CT, saccharin test. Morbid history of persistent wet cough, mucopurulent sputum, nasal voice, difficult nasal breathing. Radiography of the paranasal sinuses showed signs of pansinusitis. At pulmonary CT, there were characteristic signs of chronic broncho-pulmonary processes - varicose and sac-shaped bronchiectasis, pleuro-pulmonary adhesions, fibro-atelectatic areas in various segments. Spirometry – moderate and severe restrictive and obstructive disorders.