Abstract
Primary cardiac tumors are extremely rare, with an incidence of 0.001–0.03%. Twenty-five percent of these tumors are malignant, with sarcomas accounting for approximately 95%. Cardiac intimal sarcoma is the least reported subtype of primary cardiac sarcoma. These endocardial mesenchymal tumors most often arise from great arterial vessels, and are rarely located in the heart. They often present with an aggressive clinical course and have a poor prognosis, with surgical resection with achievement of free margins being the mainstay of treatment. This emphasizes the importance of an early, correct diagnosis and timely intervention. We report a 60-year-old Caucasian male with several former cardiac surgical procedures due to congenital aortic stenosis, presenting with functional mitral stenosis/insufficiency and left ventricular outflow tract obstruction (LVOTO) due to massive masses in the left ventricle and atrium of the heart. Hybrid imaging with 2-deoxy-2-[18F]fluoro-D-glucose positron emission tomography/computed tomography (2-[18F]FDG PET/CT) was performed prior to surgery to characterize the intracardiac masses and estimate tumor burden, as well as to identify a potential extracardiac primary malignancy.
Highlights
Primary cardiac tumors are extremely rare, with an incidence of 0.001–0.03%
First-line imaging at the primary hospital with transesophageal echocardiography protein (CRP; 129 mg/L) and lactate dehydrogenase (LDH; 263 U/L), and an international normalized (TEE) demonstrated a massive thrombus/tumor mass adjacent to the mitral valve expanding into the ratio (INR) of 2.5
First-line imaging at the primary hospital with transesophageal echocardiography (TEE) demonstrated a massive thrombus/tumor mass adjacent to the mitral valve expanding into the left ventricular outflow tract, with physiology consistent with mitral stenosis/insufficiency and left ventricular outflow tract obstruction (LVOTO)
Summary
Primary cardiac tumors are extremely rare, with an incidence of 0.001–0.03%. Twenty-five percent of these tumors are malignant, with sarcomas accounting for approximately 95%. PET/CT) was performed prior to surgery to characterize the intracardiac masses and estimate tumor burden, as well as to identify a potential extracardiac primary malignancy. First-line imaging at the primary hospital with transesophageal echocardiography protein (CRP; 129 mg/L) and lactate dehydrogenase (LDH; 263 U/L), and an international normalized (TEE) demonstrated a massive thrombus/tumor mass adjacent to the mitral valve expanding into the ratio (INR) of 2.5.
Sign-in/Register to view highlights & summary Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callDisclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
