Prenatal and Postnatal Management of a Patient with Pentalogy of Cantrell and Left Ventricular Aneurysm

Abstract

Introduction: Omphalocele is often associated with cardiac diverticulum in the pentalogy of Cantrell, however a prenatal diagnosis of omphalocele has not been described with a broad-based, thin-walled aneurysm of the ventricular wall in a surviving patient. Case Report: A case of omphalocele with Morgagni hernia and left ventricular aneurysm diagnosed at 21 weeks, 6 days’ gestational age is reported. Initial ultrasound examination demonstrated the cardiac defect and subsequent ultrasounds revealed the abdominal wall defect. Prenatal monitoring included serial ultrasound and echocardiography. A viable fetus was delivered via cesarean section at 37 weeks’ gestational age. The omphalocele and Morgagni hernia were repaired on the infant’s 4th day of life. The cardiac defect continues to be monitored with echocardiography at 15 months of age. Discussion: The case is discussed along with a short review of the literature of midline thoracoabdominal defects and left ventricular apical aneurysms.