Abstract
An 11-year-old girl rapidly developed weakness limited to facial and shoulder muscles with associated myoedema. The legs were not involved. Electromyography demonstrated myopathic motor unit potentials and increased muscle irritability. Serum enzyme levels were markedly elevated and returned towards normal with steroid therapy although clinical improvement was slight. Two muscle biopsies showed inflammatory reaction and necrosis. The short clinical course, absence of affected family members, and laboratory findings were consistent with a restricted polymyositis. Restricted muscle involvement simulating facio-S scapulohumeral dystrophy is an unusual variation of polymyositis.
Sign-in/Register to access full text options 
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callDisclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
