Plexiform schwannoma at an unusual site involving the angle of mouth: Report of a rare case

Abstract

Plexiform schwannoma (PS) is a rare benign encapsulated peripheral nerve sheath tumor characterized by a plexiform pattern of intraneural growth often with a multinodular appearance. It usually presents as a solitary mass with a strong predilection for young adults between 20 and 50 years. Despite its common presentation in the head and neck region, involvement of the lip is extremely rare. Multiple cutaneous PSs are commonly associated with Neurofibromatosis type 2 or Schwannomatosis. To date, only a few cases of PS involving the lip have been reported. Here in we report another unusual case of PS involving the angle of mouth which was removed completely by surgical excision without any recurrence seen at 1-year post-surgery.