Abstract
A 15-year-old boy presented with swelling in the submandibular region. X-ray of the swollen part showed faint radio opaque shadow. A provisional diagnosis of sialadenitis with sialolithiasis was made. Excised mass was reported histopathologically as plexiform neurofibroma of submandibular salivary gland.Plexiform neurofibroma of the salivary gland is a rare benign tumor often present in the parotid gland. It is very rare in submandibular salivary gland. It is a slow growing, locally infiltrating tumor.
Highlights
Neurofibromas constitute only 0.4% of all salivary neoplasms
Plexiform neurofibromas of the salivary glands are rare, usually presenting in the parotid gland. They are very rare in submandibular salivary gland
Plexiform neurofibromas are frequently seen in patients with Type I neurofibromatosis and undergo malignant changes in 2% of the cases
Summary
Plexiform neurofibromas of the salivary glands are rare, often presenting in the parotid gland. They are very rare in submandibular salivary gland.[1,2] They are slow growing, locally infiltrating tumors. Five cases are reported so far in the literature.[3] Probably this is the sixth one. We are presenting this case because of its rarity of presentation. A firm swelling in the submandibular region of size 8 x 5 cm, with ovoid shape and well-defined borders was present.
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