Pleural Effusion in Limited Cutaneous Systemic Sclerosis : A Report

Abstract

Systemic sclerosis (SSc) is a chronic autoimmune multisystem disorder characterized by endothelialdysfunction and fibroblast dysfunction, which results in progressive fibrosis of the skin and internalorgans more frequently the lungs and gastro intestinal tract. Pulmonary involvement is common in thecourse of SSc, with Interstitial Lung Disease (ILD) and Pulmonary Arterial Hypertension (PAH) alongwith pleural effusion being the leading causes of death. Here we report, case of an elderly male patientpresenting with cutaneous SSc with multiple uncommon pulmonary manifestations like ILD with rightsided pleural effusion with hepatic cyst.