Persistent primitive hepatic venous plexus in a child with scimitar syndrome

Abstract

A 9-year-old girl diagnosed of scimitar syndrome was referred to our centre for evaluation and therapy. Cardiac catheterisation showed an interrupted inferior caval vein, connected by an extensive racemose network of venous channels to the hepatic veins (Fig. 1). Right pulmonary veins drained at the junction cava vein and plexus (Fig. 2). Persistent primitive hepatic venous plexus is an exceptional finding, frequently associated with interrupted or hypoplastic hepatic segment of the inferior caval vein, and congenital heart disease (pulmonary venous return anomalies often) [1].