Persistent Cloaca associated with Unilateral Lung Agenesis- A Rare Presentation

Amit Mohanrao Uttarwar,Mitesh Bachani,Jaishri Ramji,Rakesh S Joshi,Ds Rathore

doi:10.47338/jns.v3.86

Abstract

We report a case of full term female child having persistent cloaca who was diagnosed to have right lung agenesis on investigations.

Highlights

Persistent cloaca comprises of about 10% of all cases of anorectal malformation
We did a diagnostic bronchoscopy that revealed complete absence of right main bronchus and trachea continued as a single left bronchus with normal distal branching confirming the diagnosis of right lung agenesis
Schneider classified Congenital underdevelopment of the lungs as (1) Agenesis: the complete absence of the carina and the main bronchus, the lung, and the pulmonary vasculature; (2) Aplasia: the carina and the rudimentary bronchus are present, the pulmonary vessels and the alveolar tissue are absent; and (3) Hypoplasia: an ill-defined bronchus is capped by underdeveloped alveolar tissue

Summary

Introduction

Persistent cloaca comprises of about 10% of all cases of anorectal malformation. More than 80% of all patients have associated urological anomalies. Patients with long channel cloaca have a high frequency of complex associated anomalies. The most common urological anomalies are renal agenesis, renal dysplasia, vesicoureteral reflux and megaureter.

Results

Conclusion