Abstract
Perirenal lymphatic malformation (LM) is a rare benign lesion that often simulate as perinephric collection or parapelvic cyst. A neonate, antenatally diagnosed with a renal cystic mass, was investigated to have a perirenal LM on postnatal ultrasonography and MRI. The LM was excised successfully. Histopathologic examination of the specimen confirmed the diagnosis. Perirenal LM should be evoked for a renal cystic mass diagnosed prenatally. Knowledge of this entity can prevent an unnecessary nephrectomy.
Highlights
lymphatic malformation (LM) is a benign lesion, seen in children, and mainly located in the neck and axillary regions.[1]
We report a case of prenatally diagnosed renal cyst, which turned out as perirenal cystic LM
The result is a dilatation of lymphatic ducts around the kidneys and the formation of unilocular or multilocular cystic mass
Summary
LM is a benign lesion, seen in children, and mainly located in the neck and axillary regions.[1] It is classified as macrocystic, microcystic and mixed based on the size of the cysts. The prenatal ultrasound showed a unilateral cystic renal mass. The sonographic examination showed a retroperitoneal septated cyst measuring 8×5cm and pressing the right kidney and the liver. The mass was located in the perirenal space It was composed of voluminous cystic lesion filled with clear fluid (Fig. A). The cells lining the cystic space stained positive for factor-VIIIrelated antigen and CD34 and negative for keratin. No recurrence was noted on follow-up of 8 months
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