Perioperative anaesthetic management of phaeochromocytoma associated with uncorrected tetralogy of Fallot.

Abstract

The incidence of congenital heart disease among all live births in India is reportedly 0.5–0.8% of which tetralogy of Fallot (TOF) is the second most common (17.86%).[1] Paraganglioma accounts for approximately 0.1% of the hypertensive Indian population with an overall incidence of 1–2/million.[2] Both diseases are relatively uncommon and their concurrent occurrence is exceptionally rare. Only two cases of phaeochromocytoma with uncorrected TOF have been reported from India.[1,3] We have described the pertinent anaesthetic considerations in the perioperative management of surgical excision of phaeochromocytoma with unrepaired, unpalliated TOF.