Perineal groove-a rare congenital defect of perineum

Abstract

Perineal groove is rare a congenital malformation usually affects female newborn. This is characterized by a red and wet groove lined with nonepithelized mucous membrane in the perineum between the posterior fourchette and the anterior margin of anal orifice. it is usually misdiagnosed as dermatitis, perineal trauma, or infection. Less than twenty-five cases have been reported in medical literature. We are reporting a case of congenital perineal groove and literature has been reviewed to improve the recognition and management of this rare anomaly.