Perforáló dermatosisok áttekintése, fókuszban a Kyrle betegség

Abstract

Four major forms of primary perforating dermatoses have been described. Diagnostic workup may be challenging, the highly advised skin biopsy demonstrates the transepidermal elimination of dermal connective tissue. Hyperkeratosis follicularis et parafollicularis in cutem penetrans also known as “Kyrle’s disease”, is classified as a subtype of acquired perforating dermatoses. Kyrle’s disease is extremely rare in children and is often associated with underlying chronic conditions.