Abstract
Congenital hepatic arterio-venous malformations (AVM) are rare vascular anomalies and have rarely been reported in the presence of congeni-tal heart disease. The reported cases are mostly hemangiomas fed either by the hepatic artery itself or by one of its branches. We present two unique hepatic AVM cases in the presence of congenital heart defects in which the AVM was not fed by the hepatic arterial system. Transcatheter coil embolisation was successfully carried out in both of them by using non-detachable Gianturco coils. Complete occlusion was achieved without any sequel.
Highlights
Hepatic vascular malformations comprise about 10% of all cases of abnormal vascular connections within the hepatic parenchyma [1]
Hepatic arterio-venous malformation (AVM) should be differentiated from the benign hepatic vascular tumors (HVT) when an AVM can occur within the tumor mass itself
Hepatic AVMs have been reported in association with hemangiomas, and hereditary hemorrhagic telangiectasia but rarely been reported in association with congenital heart defects
Summary
Hepatic vascular malformations comprise about 10% of all cases of abnormal vascular connections within the hepatic parenchyma [1] These are further classified into fast-flow (AVMs, arterio-portal fistulas), slow-flow (porto-systemic shunts, venous lymphatic malformations) and combined forms [2]. HVT are derived from mesenchymal tissue elements and are classified as hemangioendothelioma (HE) or cavernous hemangioma (HC) [4,5] These tumors are classified into infantile hemangioendothelioma (IHE) and arteriovenous malformations (AVM). Hepatic AVMs have been reported in association with hemangiomas, and hereditary hemorrhagic telangiectasia but rarely been reported in association with congenital heart defects. We encountered two such cases which are briefly described
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