Abstract
Pentalogy of Cantrell (PC) is a congenital anomaly characterized by a defect in the lower sternum, anterior diaphragm, and anterior abdominal wall; ectopia cordis; and congenital heart disease. It is a very rare congenital anomaly and the prenatal diagnosis is possible in the beginning of second trimester of pregnancy using the conventional ultrasonography. The prognosis is poor with high rates of perinatal mortality. We present a case report of prenatal diagnosis of PC at 22 weeks and 3 days of gestation. We emphasize the prenatal care follow up in a tertiary reference center, the parental counseling, the planning of delivery, and the management of newborn by a multidisciplinary team, including the description of immediate postnatal surgical repair.
Highlights
Pentalogy of Cantrell (PC) is a congenital anomaly characterized by a defect in the lower sternum, anterior diaphragm, and anterior abdominal wall; ectopia cordis; and congenital heart disease (CHD) that was first described in 1958 by Cantrell [1]
There are no studies assessing the best mode of delivery in cases of PC because this is a rare congenital anomaly with poor prognosis for which pregnancy termination is indicated in many countries
The authors opted for an early correction of ectopia cordis because of the presence of a minor CHD
Summary
Pentalogy of Cantrell: Prenatal Diagnosis, Delivery, and Immediate Postnatal Surgical Repair. Edward Araujo Júnior 1,* Milene Carvalho Carrilho 1, Bruno Rodrigues Toneto 1, José Cícero Stocco Guilhen. How to cite: Araujo Júnior E, Carrilho MC, Toneto BR, Guilhen JC. Pentalogy of Cantrell: Prenatal diagnosis, delivery, and immediate postnatal surgical repair.
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