Pecoma cervical - a propósito de um caso clínico

Abstract

PEComas (“perivascular epithelioid cell diferentiation tumors”) are mesenchymal tumours, usually benign, extremely rare, composed of perivascular epithelioid cells, with distinctive histologically and immunohistochemically characteristics. They are described in lung, kidney and liver, but are extremely rare in head and neck. The pertinence of this report is due to the rarity of this tumour and the difficulty of reaching a final diagnosis. Clinic case: Patient 34 years old, male, referring a right cervical mass for one year, painless, with little growth, and no other symptoms. The observation revealed a right cervical tumour of 10 cm of diameter at the trapezium fossa. The palpation is painless, and the tumour is soft, smooth, not pulsating, and not fixed. The patient does a cervical CT scan and a cervical MRI. He is taken to surgery, with total excision of the tumour. There is no post-surgery morbility. The final histopathological diagnosis is PEComa. The authors discuss histological and immunohistochemical criteria that led to this final diagnosis.