Partial nephrectomy can be a successful treatment option for renal epithelioid angiomyolipoma: a case report and literature review.

Abstract

Renal epithelioid angiomyolipoma is arare tumour which involves kidneys in most cases. It is known for its aggressive behaviour as asignificant number of cases have been associated with metastatic epithelioid angiomyolipoma. Usually, radical treatment with systemic therapy is recommended. Only asmall number of cases of epithelioid angiomyolipomas have been reported with thestandard treatment being radical or partial nephrectomy. We present a case report showing that partial nephrectomy can be asuccessful treatment option for renal epithelioid angiomyolipoma. This is thefirst case of this nature in Lithuania. In this case, a40-year-old male with epithelioid angiomyolipoma of theleft kidney is presented. In 2012, acystic left renal mass 40×41mm in size was diagnosed incidentally while performing ultrasound and later confirmed by MRI. Due to thesize of thetumour and thepossibility of renal cell carcinoma, surgery was scheduled. Left partial nephrectomy was performed successfully. Final pathology report came back with thediagnosis of renal epithelioid angiomyolipoma. Thepatient had yearly follow-up for six years by CT scan, and neither recurrence nor progression were observed. Early detection and diagnosis are crucial for treatment as thetumour tends to have malignancy potential. With early diagnosis, partial nephrectomy can be performed with yearly follow-up and no systemic treatment required.