Parry Romberg Syndrome: A Case Report Involving Intranasal Mucosal Atrophy and Secondary Eustachian Tube Dysfunction

Abstract

Parry Romberg syndrome is a rare disorder described as facial asymmetry. It is of unknown aetiology, but trophic malfunction of the sympathetic system has been proposed as a cause. The syndrome results in specific soft tissue, skeletal, dental and skin changes in the affected side of the face, with or without neurological signs and symptoms.The case we present here is a 23 year old female with Parry Romberg syndrome. Clinically she has left sided facial atrophy affecting both the soft tissue and the bone structure. The patient received pharmacological and surgical treatments to slow the progression and correct the contour of her face. She complained lately from autophony, which is the unusual loud hearing of a person's own voice and own breathing. A diagnostic nasoendoscopy showed atrophied nasal mucosa and Eustachian tube dysfunction which has never been described before to be secondary to parry Romberg syndrome.