Abstract
Papuloerythroderma of Ofuji was first described by Ofuji in 1984. This rare entity is characterized by presence of polygonal, erythematous to brown papules, covering the entire body surface, with a characteristic sparing of body folds (deck chair sign). On hematological investigations, there is characteristic eosinophilia with lymphopenia. It may or may not be associated with underlying malignancies. We report a case of a 81 year male patient where a diagnosis of Papuloerythrodrma secondary to non-Hodgkin`s lymphoma was made based on the criteria laid by Torchia et Al. Our patient satisfied 4 out of 5 major criteria and all 5 of the minor criteria. This case is reported because of its rarity and characteristic clinical presentation.
Highlights
Papuloerythroderma of Ofuji is a distinct clinical entity described by Ofuji in 1984 after observing 4 cases with similar presentations.[1]
We report a case of an elderly male with classical cutaneous and hematological features of papuloerythroderma with associated non Hodgkin’s lymphoma
Jagati A, et al Papuloerythroderma with associated non- Hodgkin's lymphoma coalesced at some places to form plaques covering almost 90 % of body areas (Fig 1)
Summary
Papuloerythroderma of Ofuji is a distinct clinical entity described by Ofuji in 1984 after observing 4 cases with similar presentations.[1] There were solid flat topped, erythematous to brownish pruritic papules present extensively over entire trunk and extremities and typically sparing the flexural areas It was seen more commonly in elderly males. Clinical possibilities of papuloerythroderma of Ofuji; cutaneous T cell lymphoma; leukemia cutis and Kimura’s disease were considered, and patient was admitted for further management. On hematological examination, his peripheral blood smear showed leukocytosis of total leukocyte count of 22,300 with eosinophilia (36%) with relative lymphopenia (2%). The patient did not visit an oncologist and succumbed after 1 month
Sign-in/Register to view highlights & summary Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callMore From: Nepal Journal of Dermatology, Venereology & Leprology
Disclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
