Papillon–lefevre syndrome: A dilemma for the dentist

Abstract

Papillon–Lefevre syndrome (PLS) is a rare autosomal recessive disorder characterized by palmoplantar keratinization and premature loss of both primary and permanent dentition. Patients are often edentulous at an early age. Therefore, the dentist should be aware of the same because an early diagnosis of the syndrome can help preserve the teeth by early institution of treatment, using a multidisciplinary approach. Here, we present a case of PLS, along with a comprehensive review of the etiology, clinical features, and management of the condition.