P61 Improving the detection and management of pulmonary exacerbations in children with primary ciliary dyskinesia by designing and implementing a written self- management plan

Abstract

IntroductionPrimary ciliary dyskinesia (PCD) is a rare, inherited disorder of motile cilia, predisposing patients to repeated respiratory infections. These pulmonary exacerbations (PEx) cause significant morbidity, and prompt treatment with antibiotics...