Abstract

Pulmonary function tests are the gold standard for evaluating disease status and treatment response in persons with cystic fibrosis (CF). Pulmonary function, however, is an outcome influenced by multiple circumstances. Sweat chloride (SwCl) concentration is a reliable outcome, solely reflecting the activity of the CF transmembrane conductance regulator protein. In the present study, we aim to evaluate the effect of ETI treatment on SwCl concentration.

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