Osteofibrous Dysplasia of Humerus: An Unusual Presentation of a Rare Lesion

Abstract

Osteofibrous dysplasia (OFD) is a benign fibro-osseous lesion, and it comprises 0.2% of all primary bone tumors. It occurs most commonly in infancy and childhood and most commonly involves the tibia/fibula. The most frequent site is the cortical bone of the anterior midshaft of the tibia, and involvement of other long bones, such as the humerus, ulna, radius, and clavicle are extremely rare. It is usually managed conservatively but surgical intervention is needed in cases with a pathological fracture or significant deformity. We report a rare case of OFD in a 7-year-old male child occurring in the meta-diaphyseal region of the proximal humerus, with recurrence of the lesion and secondary aneurysmal bone cyst (ABC) changes who underwent three surgical procedures and still has a persistent residual lesion.